セリーヌ・ディオンさん「まれな神経疾患」公表　公演中止

【パリＡＦＰ＝時事】カナダの歌手セリーヌ・ディオンさんが８日、「非常にまれな神経疾患」が原因で歌唱に支障が出ているとして、欧州公演の延期や中止を発表した。（写真は、カナダ人歌手のセリーヌ・ディオンさん）
　ディオンさんはインスタグラムに５分間の動画を投稿。フランス語と英語で、声を震わせながら「長い間」健康問題に悩まされてきたとし、「最近、１００万人に１人ほどの割合で発症する『スティッフパーソン症候群』と呼ばれる非常にまれな神経疾患と診断された」と語った。
　同症候群が引き起こす筋攣縮（れんしゅく）により「時には歩くのも困難になり、今までのように声帯を使って歌うこともできなくなるなど、日常生活のあらゆる面に影響が出ている」と説明。子どもたちや医師団に支えられながら日々、症状の改善に努めているが「苦闘している」と吐露し、「私は歌うことしか知らない。人生をかけてやってきたことで、最も愛していること」だと語った。
　ディオンさんは今年、筋攣縮を理由に欧州ツアーを延期していた。来年２月からチェコで始まる予定だった同ツアーは、春までの公演が２０２４年に延期され、夏の８公演は中止となった。８月下旬～１０月の公演予定には今のところ変更はない。【翻訳編集ＡＦＰＢＢＮｅｗｓ】
〔ＡＦＰ＝時事〕（2022/12/09-18:02）

Stiff-person syndrome, which has forced Canadian superstar singer Celine Dion to postpone her European tour, is a very rare neurological condition that causes progressive muscle stiffness as well as muscle spasms.
Around one in a million people are estimated to have the condition, according to the US National Organization for Rare Disorders (NORD).
Symptoms develop over a matter of months or years, normally between the ages of 30 to 60, and can remain stable in some cases or get gradually worse in others.
The often painful muscle spasms last minutes or even hours and can happen randomly or be triggered by events such as loud noises, light physical contact, stress or situations requiring a heightened emotional response, NORD said.
If left untreated, the syndrome can cause problems walking leading to the use of a wheelchair, and can significantly impact a person's ability to carry out daily tasks.
While we're still learning about this rare condition, we now know this is what's been causing all of the spasms I've been having, an emotional Dion said in an Instagram post on Thursday in which she also postponed or cancelled planned concerts across Europe.
Unfortunately, the spasms affect every aspect of my daily life, sometimes causing difficulties when I walk and not allowing me to use my vocal cords to sing the way I'm used to, she added.
- Often misdiagnosed -
The condition was first identified in 1956, and was dubbed stiff-man syndrome. The name has since been changed -- women in fact make up a majority of cases.
The exact cause remains unknown, though it is thought to be an autoimmune disorder that sometimes occurs alongside other autoimmune conditions.
Stiff-person syndrome can be diagnosed by testing for certain antibodies, for example GAD antibodies, and via an electromyography procedure which evaluates electrical activity in muscles.
However the syndrome is commonly misdiagnosed as a range of non-neurological conditions, according to US-based research published earlier this week.
Improved diagnostic accuracy will reduce exposure to unnecessary treatments and health care costs, the researchers wrote in the journal Neurology.
The only available treatments aim to manage the symptoms, for example commonly available drugs that lessen muscle stiffness and spasms.
Stretching, massage, acupuncture and other non-drug therapies are also often part of the mix, according to NORD.
I have a great team of doctors working alongside me to help me get better, Dion said on Instagram.
I'm working hard with my sports medicine therapist every day to build back my strength and my ability to perform again.